Darier's disease


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Related to Darier's disease: lichen planus
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Synonyms for Darier's disease

a rare hereditary condition marked by dark crusted patches (sometimes containing pus)

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References in periodicals archive ?
Hoogendoorn et al., "ATP2A2 mutations in Darier's disease and their relationship to neuropsychiatric phenotypes," Human Molecular Genetics, vol.
Pemphigus Desmosomes Psoriasis Increased T-cell activity Darier's disease Gene encoding Autosomal intracellular dominant calcium pump (ATP2A2 gene) gene) Dyskeratosis Dyskerin (X-linked), X-linked, congenita TINF2 and sometimes TERT (autosomal autosomal dominant) dominant Disorders Clinical features Histopathological features Defect in [alpha]-helical rod pattern Epidermolysis Blistering of hands and Intraepithelial bullosa simplex feet which heal clefting without scarring.
Darier's disease occurs worldwide, with an estimated incidence of 4 per million per decade (3) and an estimated prevalence ranging from 1 in 30,000 (4) to 1 in 100,000.
Sonia Freeman, who suffers with the rare skin condition Darier's disease, with husband Leigh PICTURE: Andrew Davies [umlaut]
A history of eczema, atopic dermatitis (regardless of disease severity or activity), or Darier's disease is a risk factor for EV, both for vaccine recipients and their close contacts; having household contacts with any of these conditions also is a contraindication Although no data exist to predict the risk for EV among such persons, before 1990, the incidence rate for EV after smallpox vaccination was approximately eight to 80 cases per 1 million vaccinations (8).
Intracellular persistence of Staphylococcus aureus small-colony variants within keratinocytes: a cause tot antibiotic treatment failure in a patient with Darier's disease. Clin Infect Dis 2001;32:1643-7.
Further, because of the increased risk of inadvertent inoculation, people with other acute, chronic, or exfoliative skin conditions--such as burns, impetigo, varicella zoster, herpes, severe acne, or psoriasis--are also excluded, as are those with Darier's disease, a hereditary blistering disorder.
Inflammatory linear verrucous epidermal nevus Linear epidermal nevus Linear psoriasis Linear lichen planus Linear verruca plana Linear porokeratosis Linear Darier's disease Blaschkitis
Darier's disease may look similar to cases of CARP without pigmentary change, but it often will have accompanying nail changes.
Darier's disease was first described by a French dermatologist, Jean D rier, and an American dermatologist, James C.
Rare consequence of HHD is squamous-cell carcinoma.[12] The differential diagnoses of Hailey-Hailey disease included fungal infection, intertrigo, psoriasis, extramammary Paget's disease, acanthosis nigricans, pemphigus vegetans and Darier's disease. Histopathology of early lesions shows lacunae formed by suprabasilar clefting with acantholytic cells either singly or in clumps lining the clefts.
Splinter hemorrhages may also be associated with mitral stenosis, vasculitis, cirrhosis, trichinosis, scurvy, chronic glomerulonephritis, and Darier's disease. However, due to the diverse and common causes of splinter hemorrhages, they cannot be used as an isolated sign of illness, except when they are accompanied by things like fever, Roth's spots, Osler's nodes, Janeway's lesions, or a heart murmur, since any of the above would greatly increase their significance.