Krabbe's or globoid
cell leukodystrophy also has predominant periventricular white matter involvement, but also has hypointense thalami due to calcifications (12) and early cerebellar involvement seen as alternating halos.
Among these, the most frequent were discoid (23%), globoid
(20%), and conical (16%).
cell leukodystrophy (GLD) or Krabbe disease (KD) is an inherited neurodegenerative lysosomal enzyme disorder affecting the central and peripheral nervous systems.
Greater numbers of globoid
, discoid, and vein galls were found in the interior than on the border of the tree crown (Leite et al.
Deeply eosinophilic serrated or beaded bands and globoid
structures are seen scattered in the collagenous areas.
TABLE 1 Morphological description of insect galls associated with host plant Styrax pohlii in the period of July, 2007, in a fragment of semi-deciduous forest in Goiania, Goias, Brazil Morpho Gall description -species Organ Form Color Pubescence A Leaf Globoid
Brown Pilose B Leaf Globoid
Red/Brown Pilose (erythrocyte) C Leaf (abaxial) Globoid
Brown Glabrous D Leaf Globoid
Brown Glabrous E Leaf Conicle Green Glabrous F Leaf (adaxial) Discoid Brown Glabrous G Stem Fusiform Brown Glabrous H Stem Globoid
Brown Glabrous Morpho Gall Galling Figure -species Description Ocurrence A Isolated Hymenoptera Fig.
The white rhizomes have a slightly segmented appearance from the brown margins of their outer membranes; the rhizomes are connected to small globoid
tubers up to 1/2 inch across.
The future for treatment by bone marrow transplantation for adrenoleukodystrophy, metachromatic leukodystrophy, globoid
cell leukodystrophy and Hurler syndrome.
Others include beta-thalassemia, mucopolysaccharoidosis type I (MPS); globoid
leukodystrophy (GLD); and chronic granulomatous disorder (CGD).
Bone marrow transplantation for globoid
cell leukodystrophy, adrenoleukodystrophy, metachromatic leukodystrophy, and Hurler syndrome.
It is also known as globoidal worm-gearing, globoid
or hour glass gear and has advantage versus a traditional worm gear because of increased driving efficiency with 6-10% and increased loading capacity (about 30%).
Proteins were largely present in the endosperm; diffuse before veraison, and subsequently concentrated in globoid
cell leukodystrophy, also known as Krabbe's disease, is an autosomal recessive white matter disorder caused by the deficiency of [beta]-galactocerebrosidase.
2003), a dramatic reduction in globoid
number and size (and thus of phytic acid amount) was evident in the mutant compared with the wild-type scutellum (Fig.
Mouthfuls of obscure diseases tumble from Kurtzberg's lips as though they were days of the week -- adrenoleukodystrophy, metachromatic and globoid
leukodystrophy, to name a few.