A 58-year-old male with multiple enchondromas experienced malignant degeneration of one into a chondrosarcoma of the distal femur.
2) Considered a subtype of enchondromatosis, Maffucci syndrome presents with multiple enchondromas that are associated with soft tissue hemangiomas.
Radiopharmaceutical uptake can vary greatly depending upon local reactive bone formation, ossification of the enchondromas
, and local hyperemia.
Secondary chondrosarcomas occur in preexisting benign car tilaginous neoplasms, such as a complication of a preexisting enchondroma or osteochondroma (1, 2).
The degree of endosteal scalloping is considered the best predictor in distinguishing chondrosarcoma from benign enchondroma on radiographs.
MRI findings may be useful in distinguishing enchondromas in the long bones from bone infarcts.
Conclusions: In the setting of pain with no other abnormal findings, MRI can differentiate between bone infarct and enchondromas usually, but chondrosarcoma versus enchondroma must be differentiated with biopsy.
Several lesions that can be polyostotic include multiple hereditary exostoses, enchondromas, fibrous dysplasia and, occasionally, eosinophilic granulomas.
If periostitis is present, fibrous dysplasia, solitary bone cyst, nonossifying fibromas, and enchondromas can be removed from consideration unless complicated by fracture.
On the other hand, diagnoses specific to older patients include metastasis, multiple myeloma, enchondroma, and subchondral cysts.
This is seen in lesions such as enchondroma and chondrosarcomas.
The hands and fingers were diffusely enlarged secondary to enchondromas
Magnetic resonance (MR) imaging demonstrates the enchondromas
to be well-delineated, lobulated masses that have low signal intensity on T1-weighted images and high signal intensity on T2-weighted images (Figure 4).
While the lesion is composed of benign cartilage, the appearance is more active than an enchondroma
, and may be confused with chondrosarcoma.
sometimes cause dyschondroplasia of the long bones during childhood.