A diagnosis of severe post ductal coarctation of aorta
was made and Balloon aortoplasty was planned for the patient.
Cardiac investigations revealed complex coarctation of aorta
, the commonest cardiac lesion.
Its clinical findings are similar to coarctation of aorta
(AC) or interrrupted aorta (IA) and it is manifested with findings of severe heart failure in the first hours and days of life.
4) The acquired form of coarctation of aorta
is commonly associated with inflammatory conditions like Takayasu arteritis (5) and severe atherosclerosis.
Diagnosis Frequency (n) Age in years median (IQR) * Atrial septal defect 251 32(23-32) Ventricular septal defect 126 21(17-21) Patent ductus arteriosus 8 25(18-25) Pulmonary valve stenosis 17 28(18-28) D-transposition of great arteries 30 21(19-21) L-transposition of great arteries 12 24(18-24) Fontan circulation 36 20(17-20) Coarctation of aorta
13 21(16-21) Ebstein anomaly 18 27(21-27) Tetralogy of Fallot 61 21(17-21) Bicuspid aortic valve 21 26(19-26) Atrioventricular septal defect 7 23(20-23) Overall 600 24(19-24) Diagnosis Gender male/ female (%) Atrial septal defect 38.
While combination of VSD with other anomalies like PDA and ASD were 13(20%), there were two cases of Aortic stenosis and Coarctation of aorta
As indicated previously, aneurysms involving the sinuses of Valsalva may occur in patients with coarctation of aorta
, particularly if a bicuspid aortic valve is present.
Coarctation of aorta
(localized narrowing of the aorta)
His medical history was contributory for sickle cell anemia and repair several years earlier of an aortic coarctation secondary to Shone syndrome, consisting of coarctation of aorta
, parachute deformity of mitral valve, aortic stenosis, and persistent left subclavian vein.
Isolated coarctation of aorta
has varied clinical presentations depending upon its severity and age of presentation.
1] Also known as aortic arch syndrome, pulseless disease, reverse coarctation of aorta
, Martorell disease.
His CT findings suggested grossly dilated aortic root and ascending aorta, LV hypertrophy, severe postductal coarctation of aorta
, multiple mediastinal posterior chest wall, and paravertebral and intercostal collaterals on either side bypassing coarctation with collaterals channels [Figure 1A].